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Victoria's voluntary assisted dying law: clinical implementation as the next challenge

Ben P White, Lindy Willmott and Eliana Close
Med J Aust 2019; 210 (5): . || doi: 10.5694/mja2.50043
Published online: 25 February 2019

Victoria's voluntary assisted dying law will soon come into effect; a remaining challenge is effective clinical implementation

The Voluntary Assisted Dying Act 2017 (Vic) (VAD Act) will become operational on 19 June 2019. A designated 18‐month implementation period has seen an Implementation Taskforce appointed, and work is underway on projects including developing clinical guidance, models of care, medication protocols and training for doctors participating in voluntary assisted dying (VAD).1 While some have written on the scope of, and reaction to, the VAD legislation,2,3,4 there has been very little commentary on its implementation. Yet, important choices must be made about translating these laws into clinical practice. These choices have major implications for doctors and other health professionals (including those who choose not to facilitate VAD), patients, hospitals and other health providers. This article considers some key challenges in implementing Victoria's VAD legislation.


  • Australian Centre for Health Law Research, Queensland University of Technology, Brisbane, QLD


Correspondence: bp.white@qut.edu.au

Competing interests:

Ben White and Lindy Willmott have been engaged by the Victorian Government to design and provide the legislatively mandated training for doctors involved in voluntary assisted dying. Lindy Willmott is also a member of the board of Palliative Care Australia, but this article only represents her views.

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“Better health in the bush”: why we urgently need a national rural and remote health strategy

John Wakerman and John S Humphreys
Med J Aust 2019; 210 (5): . || doi: 10.5694/mja2.50041
Published online: 25 February 2019

What are the problems in rural health service delivery and what can we do about them?

For decades, the Australian Government has been wrestling with how to “fix the rural health problem”. Long‐standing problems of workforce shortages and maldistribution, difficulties with recruitment and retention, and inadequate access to, and availability of, appropriate services persist.1 These contribute to the poor health status of many non‐metropolitan Australians, especially Aboriginal and Torres Strait Islander populations, despite the fact that governments spend millions of dollars annually on specific rural and remote health programs.2


  • 1 Flinders Northern Territory, Flinders University, Darwin, NT
  • 2 School of Rural Health, Monash University, Bendigo, VIC



Acknowledgements: 

John Wakerman receives funding from the Australian Government Department of Health, the Northern Territory Government Department of Health and the Medical Research Future Fund through the Central Australian Academic Health Science Centre.

Competing interests:

No relevant disclosures.

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Increasing registrations on the Australian Organ Donor Register

Gail Moloney, Michael Sutherland, Maddison Norton, Alison Bowling and Iain Walker
Med J Aust 2019; 210 (3): . || doi: 10.5694/mja2.50000
Published online: 18 February 2019

To the Editor: Many people are aware that Australia has an opt‐in system for recording organ donation decisions; and many are also aware that, historically, donation decisions were recorded on the driver's licence. What is not well known is that, in 2000, the Australian Organ Donor Register (AODR) was introduced as a register of consent (or objection), and that, between 2005 and 2012, the recording of donation decisions (except for South Australia) was transitioned from the driver's licence to registration on the national register, the AODR.1


  • 1 Southern Cross University, Coffs Harbour, NSW.
  • 2 Organ and Tissue Donation Service, Mid North Coast Local Health District, Coffs Harbour, NSW.
  • 3 University of Canberra, Canberra, ACT.


Correspondence: Gail.Moloney@scu.edu.au

Acknowledgements: 

This research was supported by NSW Organ and Tissue Donation Service.

Competing interests:

No relevant disclosures.

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Iodine status of Indigenous and non‐Indigenous young adults in the Top End, before and after mandatory fortification

Gurmeet R Singh, Belinda Davison, Gary Y Ma, Creswell J Eastman and Dorothy EM Mackerras
Med J Aust 2019; 210 (3): . || doi: 10.5694/mja2.12031
Published online: 18 February 2019

Abstract

Objective: To assess the median urine iodine concentration (UIC) of young adults in the Top End of Northern Territory, before and after fortification of bread with iodised salt became mandatory.

Design, setting: Analysis of cross‐sectional data from two longitudinal studies, the Aboriginal Birth Cohort and the non‐Indigenous Top End Cohort, pre‐ (Indigenous participants: 2006–2007; non‐Indigenous participants: 2007–2009) and post‐fortification (2013–15).

Participants: Indigenous and non‐Indigenous Australian young adults (mean age: pre‐fortification, 17.9 years (standard deviation [SD], 1.20 years); post‐fortification, 24.9 years (SD, 1.34 years).

Main outcome measure: Median UIC (spot urine samples analysed by a reference laboratory), by Indigenous status, remoteness of residence, and sex.

Results: Among the 368 participants assessed both pre‐ and post‐fortification, the median UIC increased from 58 μg/L (interquartile range [IQR], 35–83 μg/L) pre‐fortification to 101 μg/L (IQR, 66–163 μg/L) post‐fortification (P < 0.001). Urban Indigenous (median IUC, 127 μg/L; IQR, 94–203 μg/L) and non‐Indigenous adults (117 μg/L; IQR, 65–160 μg/L) were both iodine‐replete post‐fortification. The median UIC of remote Indigenous residents increased from 53 μg/L (IQR, 28–75 μg/L) to 94 μg/L (IQR, 63–152 μg/L; p < 0.001); that is, still mildly iodine‐deficient. The pre‐fortification median UIC for 22 pregnant women was 48 μg/L (IQR, 36–67 μg/L), the post‐fortification median UIC for 24 pregnant women 93 μg/L (IQR, 62–171 μg/L); both values were considerably lower than the recommended minimum of 150 μg/L for pregnant women.

Conclusions: The median UIC of young NT adults increased following mandatory fortification of bread with iodised salt. The median UIC of pregnant Indigenous women in remote locations, however, remains low, and targeted interventions are needed to ensure healthy fetal development.

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  • 1 Menzies School of Health Research, Darwin, NT
  • 2 Western Sydney University School of Medicine, Penrith, NSW
  • 3 Sydney Thyroid Clinic, Sydney, NSW
  • 4 Sydney Medical School, Sydney, NSW
  • 5 Food Standards Australia New Zealand, Canberra, ACT



Acknowledgements: 

This investigation was supported by the National Health and Medical Research Council (APP1046391). We acknowledge past and present study teams who traced participants and collected the data, particularly the late Susan Sayers, founder of the ABC study. We thank Victor Uguoma for his statistical advice. We especially thank the young adults in the Aboriginal Birth and Top End Cohorts and their families and communities for their cooperation and support, and all the individuals who helped in urban and rural locations.

Competing interests:

Dorothy Mackerras is employed by Food Standards Australia New Zealand, the agency that introduced mandatory iodine fortification.

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Reducing the dangers of e‐cigarettes for children: opportunities for regulation and consumer education

Ryan D Kennedy and Vanya C Jones
Med J Aust 2019; 210 (3): . || doi: 10.5694/mja2.50007
Published online: 18 February 2019

The importance of packaging, storage, and product design must be reflected by legislation

Electronic nicotine delivery systems (ENDS), including e‐cigarettes, are devices that heat a liquid (e‐liquid) that usually includes propylene glycol or vegetable glycerine, nicotine, and other constituents, such as colourants and flavourings. Nicotine is a naturally occurring toxin in tobacco plants that affects mammalian nervous and cardiovascular systems.1 E‐liquids containing nicotine are a poisoning risk because small amounts of nicotine can induce vomiting, cause seizures, and be lethal, particularly if ingested by young children.2 As Chivers and colleagues3 report in this issue of the MJA, e‐liquids may also contain a range of other toxic and dangerous constituents, including insecticides. In Australia and overseas, ENDS products are subject to regulations similar to those for tobacco products, including minimum age of purchase and restrictions on advertising.4 However, mitigating the risk of poisoning by ENDS products and their e‐liquids has not been the primary object of legislation.


  • Bloomberg School of Public Health, Johns Hopkins University, Baltimore, MD, United States


Correspondence: rdkennedy@jhu.edu

Competing interests:

No relevant disclosures.

  • 1. National Institute for Occupational Safety and Health, Centers for Disease Control and Prevention (USA). Nicotine: systemic agent. Updated 12 May 2011. https://www.cdc.gov/niosh/ershdb/emergencyresponsecard_29750028.html (viewed Dec 2018).
  • 2. Richtel M. Selling a poison by the barrel: liquid nicotine for e‐cigarettes. New York Times, 23 March 2014. https://www.nytimes.com/2014/03/24/business/selling-a-poison-by-the-barrel-liquid-nicotine-for-e-cigarettes.html (viewed Dec 2018).
  • 3. Chivers E, Janka M, Franklin P, et al. Nicotine and other potentially harmful compounds in “nicotine‐free” e‐cigarette liquids in Australia. Med J Aust 2019; 2019(210): 000–000.
  • 4. Kennedy RD, Awopegba A, De León E, Cohen JE. Global approaches to regulating electronic cigarettes. Tob Control 2017; 26: 440–445.
  • 5. Brown CJ, Cheng JM. Electronic cigarettes: product characterisation and design considerations. Tob Control 2014; 23 (Suppl 2): ii4–ii10.
  • 6. Food and Drug Administration (USA). FDA warns company for selling e‐liquids that resemble kid‐friendly foods as part of the agency's ongoing Youth Tobacco Prevention Plan [media release]. 29 Nov 2018. https://www.fda.gov/NewsEvents/Newsroom/PressAnnouncements/ucm627123.htm (viewed Dec 2018).
  • 7. Buettner‐Schmidt K, Miller DR, Balasubramanian N. Electronic cigarette refill liquids: child‐resistant packaging, nicotine content, and sales to minors. J Pediatr Nurs 2016; 31: 373–379.
  • 8. Herzog B, Kanada P. Our evening with blu: takeaways from Imperial Brands’ e‐cig event [report]. Wells Fargo Securities, equity research: tobacco. 28 Mar 2018. https://www.wellsfargoresearch.com/Reports/ViewReport/6dd7ce28-1708-4b56-9c05-cd59ca71fb40?source=WFR.COM&ght=bc605b8a-3f2e-4903‐ (viewed Dec 2018).
  • 9. Euromonitor International. Smokeless tobacco and vapour products in Australia [report]. Aug 2018. https://www.euromonitor.com/smokeless-tobacco-and-vapour-products-in-australia/report (viewed Dec 2018).
  • 10. Kong AY, Derrick JC, Abrantes AS, Williams RS. What is included with your online e‐cigarette order? An analysis of e‐cigarette shipping, product and packaging features. Tob Control 2018; 27: 699–702.
  • 11. Hua M, Talbot P. Potential health effects of electronic cigarettes: a systematic review of case reports. Prev Med Rep 2016; 4: 169–178.
  • 12. Wylie C, Heffernan A, Brown JA, et al. Exposures to e‐cigarettes and their refills: calls to Australian Poisons Information Centres, 2009–2016. Med J Aust 2019; 210: 000–000.
  • 13. Hughes A, Hendrickson RG. An epidemiologic and clinical description of e‐cigarette toxicity. Clin Toxicol 2018; 9: 1–7.

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Translating health professional education research evidence into effective continuous professional development

Ruth M Sladek, Sue McAllister and Kieran M Walsh
Med J Aust 2019; 210 (3): . || doi: 10.5694/mja2.12111
Published online: 18 February 2019

Biases and assumptions often arise from past experiences and, when unquestioned, can negatively influence the development of effective educational strategies

Knowledge is frequently considered as the panacea for all ills, and its acquisition is often proposed as the solution for ensuring we deliver the best quality health care. For example, training and continuing professional development (CPD) have been proposed as the first steps for medical colleges to address some troubling variations in health care practice in Australia.1 However, while proposing educational strategies to address health outcomes is logical, appropriate and defensible, it is well established that “knowing” something is quite different from “doing” something.2 Nevertheless, CPD curricula are frequently limited to “knowing”.3 While knowledge is a key prerequisite to transforming practice, how do we maximise CPD effectiveness as a strategy to improve care? And is changing individual practice through education all that is needed to change health practices and outcomes?4


  • 1 Prideaux Centre for Research in Health Professions Education, Flinders University, Adelaide, SA
  • 2 University of Sydney, Sydney, NSW
  • 3 BMJ Learning, London, UK



Competing interests:

No relevant disclosures.

  • 1. Francombe H, Buchan HA, Duggan A. Health care variation: the next challenge for clinical colleges. Med J Aust 2017; 207: 277–278. https://www.mja.com.au/journal/2017/207/7/health-care-variation-next-challenge-clinical-colleges
  • 2. Le Maistre C, Paré A. Learning in two communities: the challenge for universities and workplaces. Journal of Workplace Learning 2004; 16: 44–52.
  • 3. Boud D, Hager P. Re‐thinking continuing professional development through changing metaphors and location in professional practices. Stud Contin Educ 2012; 34: 17–30.
  • 4. Whitehead C, Kuper A, Webster F. The conceit of curriculum. Med Educ 2012; 46: 534–536.
  • 5. Greenhalgh T, Howick J, Maskrey N et al. Evidence based medicine: a movement in crisis. BMJ 2014; 348: g3725.
  • 6. Schuwirth LWT, Durning SJ. Educational research: current trends, evidence base and unanswered questions. Med J Aust 2018; 208: 161–163. https://www.mja.com.au/journal/2018/208/4/educational-research-current-trends-evidence-base-and-unanswered-questions
  • 7. Hager P. Metaphors of workplace learning: more process, less product. Fine Print 2004; 27: 7–10.
  • 8. Husmann PR, O'Loughlin VD. Another nail in the coffin for learning styles? Disparities among undergraduate anatomy students’ study strategies, class performance, and reported VARK learning styles. Anat Sci Educ 2018; https://doi.org/10.1002/ase.1777. [Epub ahead of print]
  • 9. Bohmer RM, Edmonson AC. Organizational learning health care. Health Forum J 2001; 44: 32–35.
  • 10. Lingard L. What we see and don't see when we look at “competence”: notes on a god term. Adv Health Sci Educ Theory Pract 2009; 14: 625–628.
  • 11. McAllister S, Lincoln MI, Ferguson A et al. A systematic program of research regarding the assessment of speech‐language pathology competencies. Int J Speech Lang Path 2011; 13: 6, 469–479.
  • 12. Edmondson AC. Learning from failure in health care: frequent opportunities, pervasive barriers. Qual Saf Health Care 2004; 13 (Suppl): ii3–ii9.
  • 13. Allegranzi B, Gayet‐Ageron A, Damani N et al. Global implementation of WHO's multimodal strategy for improvement of hand hygiene: a quasi‐experimental study. Lancet 2013; 13: 843–851.
  • 14. van Merrienboer JJ, Sweller J. Cognitive load theory in health professional education: design principles and strategies. Med Educ 2010; 44: 85–93.
  • 15. Hattie JAC. Visible learning: a synthesis of over 800 meta‐analyses relating to achievement. London, UK: Routledge; 2009.

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Emerging diabetes and metabolic conditions among Aboriginal and Torres Strait Islander young people

Angela Titmuss, Elizabeth A Davis, Alex Brown and Louise J Maple‐Brown
Med J Aust 2019; 210 (3): . || doi: 10.5694/mja2.13002
Published online: 18 February 2019

Intersectoral collaboration is needed to engage communities and design effective culturally and age‐appropriate interventions

The gap between the health of Aboriginal and Torres Strait Islander and non‐Indigenous Australians is well documented, with many policies and programs currently working towards improving outcomes. Despite these efforts, life expectancy is 10–11 years less than that of non‐Indigenous Australians,1 and 65% of deaths occur before 65 years of age, compared with 19% in the non‐Indigenous population.1

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  • 1 Royal Darwin Hospital, Darwin, NT
  • 2 Menzies School of Health Research, Darwin, NT
  • 3 Princess Margaret Hospital for Children, Perth, WA
  • 4 Aboriginal Health Research Accord, South Australian Health and Medical Research Institute, Adelaide, SA
  • 5 University of South Australia, Adelaide, SA



Acknowledgements: 

We acknowledge other members of the Hot North Diabetes in Youth collaboration (Northern Australia Tropical Disease Collaborative Research Program, NHMRC project grant 1131932): Peter Azzopardi, Elizabeth Barr, Paul Bauert, Gavin Cleland, Christine Connors, James Dowler, Sandra Eades, Keith Forrest, Aveni Haynes, Renae Kirkham, Elizabeth Moore, Vicki O'Donnell, Glenn Pearson, Lydia Scott, Jonathan Shaw, Sally Singleton, Ashim Sinha and Mark Wenitong. Angela Titmuss is supported by an NHMRC Postgraduate Scholarship and RACP Woolcock Scholarship. Alex Brown is supported by an NHMRC Research Fellowship (1137563). Louise Maple‐Brown is supported by an NHMRC Practitioner Fellowship (1078477).

Competing interests:

No relevant disclosures.

  • 1. Australian Institute of Health and Welfare. The health and welfare of Australia's Aboriginal and Torres Strait Islander peoples: 2015 (AIHW Cat. No. IHW 147). Canberra: AIHW, 2015. https://www.aihw.gov.au/reports/indigenous-health-welfare/indigenous-health-welfare-2015/contents/table-of-contents (viewed Nov 2018).
  • 2. Azzopardi PS, Sawyer SM, Carlin JB, et al. Health and wellbeing of Indigenous adolescents in Australia: a systematic synthesis of population data. Lancet 2018; 391: 766–782.
  • 3. Haynes A, Kalic R, Cooper M, et al. Increasing incidence of type 2 diabetes in Indigenous and non‐Indigenous children in Western Australia, 1990‐2012. Med J Aust 2016; 204: 303. https://www.mja.com.au/journal/2016/204/8/increasing-incidence-type-2-diabetes-indigenous-and-non-indigenous-children
  • 4. Craig ME, Femia G, Broyda V, et al. Type 2 diabetes in Indigenous and non‐Indigenous children and adolescents in New South Wales. Med J Aust 2007; 186: 497–499. https://www.mja.com.au/journal/2007/186/10/type-2-diabetes-indigenous-and-non-indigenous-children-and-adolescents-new
  • 5. Stone M, Baker A, Maple‐Brown L. Diabetes in young people in the Top End of the Northern Territory. J Paed Child Health 2013; 49: 976–979.
  • 6. McGavock J, Wicklow B, Dart AB. Type 2 diabetes in youth is a disease of poverty. Lancet 2017; 390: 1829.
  • 7. Valery PC, Moloney A, Cotterill A, et al. Prevalence of obesity and metabolic syndrome in Indigenous Australian youths. Obes Rev 2009; 10: 255–261.
  • 8. Australian Bureau of Statistics. Australian Aboriginal and Torres Strait Islander Health Survey: first results, Australia, 2012‐13 (ABS Cat. No. 4747.0.055.001). Canberra: ABS, 2013. http://www.abs.gov.au/ausstats/abs@.nsf/mf/4727.0.55.001 (viewed Nov 2018).
  • 9. Dart AB, Sellers EA, Martens PJ, et al. High burden of kidney disease in youth‐onset type 2 diabetes. Diab Care 2012; 35: 1265–1271.
  • 10. Viner R, White B, Christie D. Type 2 diabetes in adolescents: a severe phenotype posing major clinical challenges and public health burden. Lancet 2017; 389: 2252–2260.
  • 11. Mendelson M, Cloutier J, Spence L, et al. Obesity and type 2 diabetes mellitus in a birth cohort of First Nation children born to mothers with pediatric‐onset type 2 diabetes. Pediatr Diabetes 2011; 12: 219–228.
  • 12. Chow E, Chan JCN. Explaining the high prevalence of young‐onset diabetes among Asians and Indigenous Australians. Med J Aust 2017; 207: 331–332. https://www.mja.com.au/journal/2017/207/8/explaining-high-prevalence-young-onset-diabetes-among-asians-and-indigenous
  • 13. Dabelea D, Hanson RL, Lindsay RS, et al. Intrauterine exposure to diabetes conveys risks for type 2 diabetes and obesity: a study of discordant sibships. Diabetes 2000; 49: 2208–2211.
  • 14. Chen P, Piaggi P, Traurig M, et al. Differential methylation of genes in individuals exposed to maternal diabetes in utero. Diabetologia 2017; 60: 645–655.
  • 15. Wheelock KM, Sinha M, Knowler WC, et al. Metabolic risk factors and type 2 diabetes incidence in American Indian children. J Clin Endocrinol Metab 2016; 101: 1437–1244.
  • 16. Dabelea D, Mayer‐Davis EJ, Lamichhane AP, et al. Association of intrauterine exposure to maternal diabetes and obesity with type 2 diabetes in youth: the SEARCH case‐control study. Diab Care 2008; 31: 1422–1426.
  • 17. Lindberg SM, Adams AK, Prince RJ. Early Predictors of Obesity and Cardiovascular Risk Among American Indian Children. Mat Child Health J 2012; 16: 1879–1886.
  • 18. Van Buren DJ, Tibbs TL. Lifestyle interventions to reduce diabetes and cardiovascular risk among children. Curr Diab Rep 2014; 14: 557–567.
  • 19. Paul CL, Ishiguchi P, D'Este CA, et al. Testing for type 2 diabetes in Indigenous Australians: guideline recommendations and current practice. Med J Aust 2017; 207: 206–210. https://www.mja.com.au/journal/2017/207/5/testing-type-2-diabetes-indigenous-australians-guideline-recommendations-and

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New guidelines from the Thrombosis and Haemostasis Society of Australia and New Zealand for the diagnosis and management of venous thromboembolism

Huyen A Tran, Harry Gibbs, Eileen Merriman, Jennifer L Curnow, Laura Young, Ashwini Bennett, Chee Wee Tan, Sanjeev D Chunilal, Chris M Ward, Ross Baker and Harshal Nandurkar
Med J Aust 2019; 210 (5): . || doi: 10.5694/mja2.50004
Published online: 11 February 2019
Correction(s) for this article: Erratum | Published online: 17 February 2020

Abstract

Introduction: Venous thromboembolism (VTE), including deep vein thrombosis (DVT) and pulmonary embolism (PE), is the third most common cardiovascular disease and, globally, more than an estimated 10 million people have it yearly. It is a chronic and recurrent disease. The symptoms of VTE are non‐specific and the diagnosis should actively be sought once considered. The mainstay of VTE treatment is anticoagulation, with few patients requiring additional intervention.

A working group of experts in the area recently completed an evidence‐based guideline for the diagnosis and management of DVT and PE on behalf of the Thrombosis and Haemostasis Society of Australia and New Zealand (www.thanz.org.au/resources/thanz-guidelines).

Main recommendations:

  • The diagnosis of VTE should be established with imaging; it may be excluded by the use of clinical prediction rules combined with D‐dimer testing.
  • Proximal DVT or PE caused by a major surgery or trauma that is no longer present should be treated with anticoagulant therapy for 3 months.
  • Proximal DVT or PE that is unprovoked or associated with a transient risk factor (non‐surgical) should be treated with anticoagulant therapy for 3–6 months.
  • Proximal DVT or PE that is recurrent (two or more) and provoked by active cancer or antiphospholipid syndrome should receive extended anticoagulation.
  • Distal DVT caused by a major provoking factor that is no longer present should be treated with anticoagulant therapy for 6 weeks.
  • For patients continuing with extended anticoagulant therapy, either therapeutic or low dose direct oral anticoagulants can be prescribed and is preferred over warfarin in the absence of contraindications.
  • Routine thrombophilia testing is not indicated.
  • Thrombolysis or a suitable alternative is indicated for massive (haemodynamically unstable) PE.

 

Changes in management as a result of the guideline: Most patients with acute VTE should be treated with a factor Xa inhibitor and be assessed for extended anticoagulation.


  • 1 Alfred Health, Melbourne, VIC
  • 2 Monash University, Melbourne, VIC
  • 3 Waitemata District Health Board, Auckland, New Zealand
  • 4 Haemophilia Treatment Centre, Westmead Hospital, Sydney, NSW
  • 5 Auckland District Health Board, Auckland, New Zealand
  • 6 Monash Medical Centre, Melbourne, VIC
  • 7 Royal Adelaide Hospital, Adelaide, SA
  • 8 Monash Health, Melbourne, VIC
  • 9  Royal North Shore Hospital, Sydney, NSW
  • 10 Perth Blood Institute, Perth, WA
  • 11 Australian Centre of Blood Diseases, Melbourne, VIC


Correspondence: huyen.tran@monash.edu

Competing interests:

No relevant disclosures.

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Current thinking in the health care management of children with cerebral palsy

David Graham, Simon P Paget and Neil Wimalasundera
Med J Aust 2019; 210 (3): . || doi: 10.5694/mja2.12106
Published online: 11 February 2019

Summary

 

  • Cerebral palsy is a developmental disorder of movement and posture which is often associated with comorbidities.
  • While there is currently a limited range of evidence‐based treatments that change the underlying pathology of cerebral palsy, there are many areas in which health care professionals can change the natural history of cerebral palsy and improve participation and quality of life for children with this condition.
  • Early identification has become of paramount importance in the management of cerebral palsy, and it is hoped that it will allow earlier access to cerebral palsy interventions that may improve the natural history of the condition.
  • Common challenges in the management of cerebral palsy include spasticity and dystonia, management of pain, hip surveillance, sleep and feeding, swallowing and nutrition.
  • The six Fs framework (function, family, fitness, fun, friends and future) provides a guide to developing shared goals with families in the management of cerebral palsy.

 


  • 1 Concord Centre for Mental Health, Sydney, NSW
  • 2 Kids Neuroscience Centre, Kids Research, Sydney, NSW
  • 3 Kids Rehab, Children's Hospital at Westmead, Sydney, NSW
  • 4 Royal Children's Hospital Melbourne, Melbourne, VIC



Competing interests:

No relevant disclosures.

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Food protein‐induced enterocolitis syndrome: guidelines summary and practice recommendations

Sam Mehr and Dianne E Campbell
Med J Aust 2019; 210 (2): . || doi: 10.5694/mja2.12071
Published online: 4 February 2019

Summary

 

  • Food protein‐induced enterocolitis syndrome (FPIES) is a poorly understood non‐IgE gastrointestinal‐mediated food allergy that predominantly affects infants and young children.
  • Cells of the innate immune system appear to be activated during an FPIES reaction.
  • Acute FPIES typically presents between one and 4 hours after ingestion of the trigger food, with the principal symptom being profuse vomiting, and is often accompanied by pallor and lethargy. Additional features can include hypotension, hypothermia, diarrhoea, neutrophilia and thrombocytosis.
  • In Australia, the most commonly reported foods responsible for FPIES are (in descending order) rice, cow's milk, egg, oats and chicken.
  • Most children with FPIES react to only one food trigger, and thus, avoidance of multiple foods is often not indicated.
  • FPIES is often misdiagnosed as sepsis or gastroenteritis. However, a diagnosis of FPIES is favoured if there is rapid resolution of symptoms within hours of presentation, an absence of fever, and a lack of a significant rise in C‐reactive protein at presentation.
  • Diagnosis is often hampered by the lack of awareness of FPIES, absence of reliable biomarkers, the non‐specific nature of the presenting symptoms, and the delay between allergen exposure and symptoms.
  • Although some national peak allergy bodies have attempted to improve the diagnosis and management of FPIES, up until 2017 there were no internationally agreed guidelines for its diagnosis and management.

 


  • 1 Royal Children's Hospital, Melbourne, VIC
  • 2 Children's Hospital at Westmead, Sydney, NSW
  • 3 University of Sydney, Sydney, NSW



Competing interests:

No relevant disclosures.

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