Volume 215 - Issue 9
Paediatric dermatofibrosarcoma protuberans: a neglected scar‐like plaque in a child
Authors: Yi‐Teng Hung, Jennifer Wu and Chun‐Yu Cheng
Med J Aust 2021; 215 (9): 404-404. || doi: 10.5694/mja2.51301
Published online: 1 November 2021
Published online: 1 November 2021
An 11-year-old girl presented with a solitary, non-tender, erythematous, indurated plaque resembling keloid slowly growing on her left upper chest for 5 years
An 11‐year‐old girl presented with a solitary, non‐tender, erythematous, indurated plaque resembling keloid slowly growing on her left upper chest for 5 years (Figure, A). Palpation examination of the lesion showed firm texture and fixity to overlying skin. Histopathology from an elliptical incisional biopsy showed a dermal tumour composed of CD34+ spindle cells arranged in a storiform fascicular pattern extending into the subcutaneous tissue (Figure, B [hematoxylin‐eosin × 40] and C [CD34 stain × 200]), confirming dermatofibrosarcoma protuberans (DFSP). She received Mohs micrographic surgery without recurrence in the 9‐month follow‐up.
Competing interests
No relevant disclosures.
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