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Paediatric dermatofibrosarcoma protuberans: a neglected scar‐like plaque in a child

Yi‐Teng Hung, Jennifer Wu and Chun‐Yu Cheng
Med J Aust 2021; 215 (9) || doi: 10.5694/mja2.51301
Published online: 1 November 2021

An 11‐year‐old girl presented with a solitary, non‐tender, erythematous, indurated plaque resembling keloid slowly growing on her left upper chest for 5 years (Figure, A). Palpation examination of the lesion showed firm texture and fixity to overlying skin. Histopathology from an elliptical incisional biopsy showed a dermal tumour composed of CD34+ spindle cells arranged in a storiform fascicular pattern extending into the subcutaneous tissue (Figure, B [hematoxylin‐eosin × 40] and C [CD34 stain × 200]), confirming dermatofibrosarcoma protuberans (DFSP). She received Mohs micrographic surgery without recurrence in the 9‐month follow‐up.

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  • 1 Chang Gung Memorial Hospital, Taoyuan, Taiwan
  • 2 Chang Gung University, Taoyuan, Taiwan


Correspondence: dermatology99999@gmail.com

Competing interests:

No relevant disclosures.

  • 1. Brennan B, Zanetti I, De Salvo GL, et al. Dermatofibrosarcoma protuberans in children and adolescents: the European Paediatric Soft Tissue Sarcoma Study Group prospective trial (EpSSG NRSTS 2005). Pediatr Blood Cancer 2020; 67: e28351.
  • 2. Llombart B, Serra‐Guillén C, Monteagudo C, et al. Dermatofibrosarcoma protuberans: a comprehensive review and update on diagnosis and management. Semin Diagn Pathol 2013; 30: 13–28.
  • 3. Durack A, Gran S, Gardiner MD, et al. A 10‐year review of surgical management of dermatofibrosarcoma protuberans. Br J Dermatol 2021; 184: 731–739.
  • 4. Hao X, Billings SD, Wu F, et al. Dermatofibrosarcoma Protuberans: Update on the Diagnosis and Treatment. J Clin Med 2020; 9: 1752.

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