Paediatric dermatofibrosarcoma protuberans: a neglected scar‐like plaque in a child

Yi‐Teng Hung, Jennifer Wu and Chun‐Yu Cheng
Med J Aust 2021; 215 (9): . || doi: 10.5694/mja2.51301
Published online: 1 November 2021

An 11‐year‐old girl presented with a solitary, non‐tender, erythematous, indurated plaque resembling keloid slowly growing on her left upper chest for 5 years (Figure, A). Palpation examination of the lesion showed firm texture and fixity to overlying skin. Histopathology from an elliptical incisional biopsy showed a dermal tumour composed of CD34+ spindle cells arranged in a storiform fascicular pattern extending into the subcutaneous tissue (Figure, B [hematoxylin‐eosin × 40] and C [CD34 stain × 200]), confirming dermatofibrosarcoma protuberans (DFSP). She received Mohs micrographic surgery without recurrence in the 9‐month follow‐up.

  • 1 Chang Gung Memorial Hospital, Taoyuan, Taiwan
  • 2 Chang Gung University, Taoyuan, Taiwan


Competing interests:

No relevant disclosures.

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